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C6

C6全稱(chēng)為補(bǔ)體成分6,是補(bǔ)體系統(tǒng)終末通路的核心分子之一,負(fù)責(zé)與C5b、C7-C9共同組裝成膜攻擊復(fù)合物,直接破壞病原體或異常細(xì)胞的脂質(zhì)膜結(jié)構(gòu)。該蛋白先天性缺陷患者易反復(fù)感染腦膜炎奈瑟菌或淋球菌,部分研究還發(fā)現(xiàn)其水平異常與妊娠期高血壓、非典型溶血尿毒綜合征等疾病相關(guān)。在自身免疫領(lǐng)域,C6過(guò)度激活可能導(dǎo)致補(bǔ)體介導(dǎo)的血管內(nèi)皮損傷,與抗磷脂抗體綜合征等病理過(guò)程存在關(guān)聯(lián)。
目前針對(duì)補(bǔ)體系統(tǒng)的藥物開(kāi)發(fā)多聚焦于上游成分(如C5抑制劑依庫(kù)珠單抗),而直接靶向C6的療法仍屬空白。2021年有研究報(bào)道了一種特異性阻斷C6功能的人源化抗體,在體外實(shí)驗(yàn)中可抑制補(bǔ)體終末通路引發(fā)的溶血反應(yīng),但尚未推進(jìn)至臨床。近年發(fā)現(xiàn)某些海洋生物毒素能選擇性干擾C6與其他補(bǔ)體蛋白的結(jié)合,為開(kāi)發(fā)新型免疫調(diào)節(jié)劑提供了線索,其轉(zhuǎn)化應(yīng)用仍需長(zhǎng)期驗(yàn)證。

熱銷(xiāo)產(chǎn)品

C6 Antibody (CSB-PA004036LA01HU)

驗(yàn)證數(shù)據(jù)

CSB-PA004036LA01HU

Western Blot
Positive WB detected in: Rat liver tissue, Mouse kidney tissue
All lanes: C6 antibody at 2.7μg/ml
Secondary
Goat polyclonal to rabbit IgG at 1/50000 dilution
Predicted band size: 105 kDa
Observed band size: 105 kDa

CSB-PA004036LA01HU

Immunohistochemistry of paraffin-embedded human kidney tissue using CSB-PA004036LA01HU at dilution of 1:100

Human Complement component C6(C6) ELISA kit (CSB-EL004036HU)

驗(yàn)證數(shù)據(jù)

CSB-EL004036HU 標(biāo)準(zhǔn)曲線

貨號(hào):CSB-EL004036HU

規(guī)格:96T/48T

靈敏度:15.6 pg/mL

檢測(cè)范圍:62.5 pg/mL-4000 pg/mL

These standard curves are provided for demonstration only. A standard curve should be generated for each set of samples assayed.

C6 Antibodies

C6 for Homo sapiens (Human)

C6 Proteins

C6 Proteins for Homo sapiens (Human)

C6 Proteins for Pan troglodytes (Chimpanzee)

C6 Proteins for Pongo pygmaeus (Bornean orangutan)

C6 Proteins for Bos taurus (Bovine)

C6 Proteins for Rattus norvegicus (Rat)

C6 Proteins for Subterranean clover stunt virus (strain F) (SCSV)

C6 ELISA Kit

C6 ELISA Kit for Homo sapiens (Human)